Vitamin/mineral and micronutrient status in patients with classical phenylketonuria

Kose E., ARSLAN N.

CLINICAL NUTRITION, cilt.38, sa.1, ss.197-203, 2019 (SCI-Expanded) identifier identifier identifier

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 38 Sayı: 1
  • Basım Tarihi: 2019
  • Doi Numarası: 10.1016/j.clnu.2018.01.034
  • Dergi Adı: CLINICAL NUTRITION
  • Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Sayfa Sayıları: ss.197-203
  • Anahtar Kelimeler: Nutrition, Phenylketonuria, Micronutrients, Phenylalanine, Vitamins, Minerals, TOTAL ANTIOXIDANT STATUS, NUTRITIONAL-STATUS, TRACE-ELEMENTS, MINERAL STATUS, PLASMA ZINC, CHILDREN, COPPER, PROTEIN, GROWTH, DEFICIENCY
  • Ankara Üniversitesi Adresli: Hayır

Özet

Background & aims: Strict low-phenylalanine diet is associated with an increased risk of developing micronutrient deficiencies in patients with phenylketonuria (PKU). The primary objective of this single center, case control study was to assess the nutritional parameters of patients with PKU on strict low-phenylalanine diet without vitamin and mineral supplementation compared to a healthy control group. Secondary objective was to identify the adequacy of vitamin/mineral supplementation in phenylalanine-free (Phe-free) amino acid formulas.