Mayer-Rokitansky-Kuster-Hauser Syndrome Accompanied by Renal Cell Carcinoma: A Case Report

Mermerkaya M., BURGU B., Hamidi N., YÜKSEL S., ÖZÇAKAR Z. B., Sertcelik A., ...Daha Fazla

JOURNAL OF PEDIATRIC HEMATOLOGY ONCOLOGY, cilt.35, sa.7, 2013 (SCI-Expanded) identifier identifier identifier

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 35 Sayı: 7
  • Basım Tarihi: 2013
  • Doi Numarası: 10.1097/mph.0b013e3182707321
  • Dergi Adı: JOURNAL OF PEDIATRIC HEMATOLOGY ONCOLOGY
  • Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Anahtar Kelimeler: Mayer-Rokitansky-Kuster-Hauser syndrome, renal cell carcinoma, renal agenesis, DIAGNOSIS
  • Ankara Üniversitesi Adresli: Evet

Özet

Mayer-Rokitansky-Kuster-Hauser anomaly originates from agenesis of the Mullerian duct including agenesis of the uterus and the vagina because of abnormal development of the uterine ducts. This syndrome may be accompanied by the upper urinary tract anomalies such as unilateral renal agenesis, ectopia of 1 or both kidneys, renal hypoplasia, horseshoe kidney, and hydronephrosis. We report a 16-year-old girl, with unilateral renal agenesis, herniating ovary, and renal cell carcinoma in her solitary kidney, associated with Mayer-Rokitansky-Kuster-Hauser syndromethe first case in the literature to our knowledge.