Two relatives with Caroli's disease
Turkish Journal of Gastroenterology, cilt.12, sa.1, ss.69-71, 2001 (Scopus, TRDizin)
- Yayın Türü: Makale / Tam Makale
- Cilt numarası: 12 Sayı: 1
- Basım Tarihi: 2001
- Dergi Adı: Turkish Journal of Gastroenterology
- Derginin Tarandığı İndeksler: Scopus, TR DİZİN (ULAKBİM)
- Sayfa Sayıları: ss.69-71
- Anahtar Kelimeler: Caroli's disease, Ursodeoxycholic acid
- Ankara Üniversitesi Adresli: Evet
Özet
Caroli's disease is characterized by congenital cystic dilatations of the intrahepatic bile ducts. The mode of inheritance of Caroli's disease is generally considered as autosomal recessive trait. Two familial cases, (a father and son) of Caroli's disease are presented, which suggest an autosomal dominant trait. Sphincterotomy was performed and ursodeoxycholic acid prescribed to these patients. The use of ursodeoxycholic acid is recommended in this patient group.