Witkop tooth and nail syndrome and orthodontics

Creative Commons License

Altug-Atac A. T., Iseri H.

Angle Orthodontist, cilt.78, sa.2, ss.370-380, 2008 (SCI-Expanded) identifier identifier identifier

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 78 Sayı: 2
  • Basım Tarihi: 2008
  • Doi Numarası: 10.2319/100406-403.1
  • Dergi Adı: Angle Orthodontist
  • Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Sayfa Sayıları: ss.370-380
  • Anahtar Kelimeler: tooth and nail syndrome, Witkop syndrome, ectodermal dysplasia, ECTODERMAL DYSPLASIA, IMPLANT METHOD, GROWTH, GIRLS
  • Ankara Üniversitesi Adresli: Evet

Özet

This case report presents the orthodontic treatment of a patient with Witkop syndrome, an autosomal dominant genetic disorder characterized by the absence of several teeth and abnormalities of the nails. The patient, a 6-year 4-month-old boy, was referred to our clinic for treatment of severe overjet and openbite. Radiographic and clinical evaluations showed peg-shaped maxillary lateral incisors and the congenital absence of three mandibular incisors as well as spoon-shaped fingernails. Treatment of openbite and overjet was initiated with functional appliances, and fixed orthodontic appliances were inserted at age 10 years 3 months. The edentulous spaces are being maintained for implants that will be provided once the patient's growth is complete. Evaluations of long-term treatment results to date have indicated improvements in both facial and dental esthetics. © 2007 by The EH Angle Education and Research Foundation, Inc.