Hypertrophic osteoarthropathy in a child with extrahepatic biliary atresia Ekstrahepatik biliyer atrezili bir çocukta hipertrofik osteoartropati

KULOĞLU Z., KANSU TANCA A., Ekici F., Demirçeken F., Tutar E., Girgin N.

Cocuk Sagligi ve Hastaliklari Dergisi, vol.47, no.3, pp.189-193, 2004 (Scopus) identifier

  • Publication Type: Article / Article
  • Volume: 47 Issue: 3
  • Publication Date: 2004
  • Journal Name: Cocuk Sagligi ve Hastaliklari Dergisi
  • Journal Indexes: Scopus
  • Page Numbers: pp.189-193
  • Keywords: Children, Extrahepatic biliary atresia, Hypertrophic osteoarthropathy, Liver failure
  • Ankara University Affiliated: Yes

Abstract

Hypertrophic osteoarthropathy (HO) is a syndrome characterized by clubbing of the fingers and toes, periosteal reaction and arthritis. It is rarely seen in childhood. There are a few reports in the literature of pediatric patients biliary atresia who developed HO. It has been suggested that pulmonary arteriovenous shunting plays an important role in the pathogenesis. Steroid and nonsteroid antiinflammatory therapy can be helpful in symptomatic patients. Here, we present a girl patient diagnosed as biliary atresia who developed HO in follow-up. We want to emphasize that children with chronic liver disease who present with finger clubbing or soft tissue hypertophy of the fingers should be a warning for hepatic hypertrophic osteoarthropathy (HHO). Furthermore, HHO should be considered in differential diagnosis in the cases of arthritis and arthralgia.