True management of Obstructed Hemi-vagina and Ipsilateral Renal Anomaly syndrome

Yakistiran B., ŞÜKÜR Y. E., Turgay B., Atabekoglu C.

TURKISH JOURNAL OF OBSTETRICS AND GYNECOLOGY, cilt.13, sa.4, ss.208-211, 2016 (ESCI) identifier identifier identifier

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 13 Sayı: 4
  • Basım Tarihi: 2016
  • Doi Numarası: 10.4274/tjod.23434
  • Dergi Adı: TURKISH JOURNAL OF OBSTETRICS AND GYNECOLOGY
  • Derginin Tarandığı İndeksler: Emerging Sources Citation Index (ESCI), Scopus, TR DİZİN (ULAKBİM)
  • Sayfa Sayıları: ss.208-211
  • Anahtar Kelimeler: Hematometrocolpos, mullerian duct anomaly, obstructed hemi-vagina and ipsilateral renal anomaly syndrome, uterus didelphys, OHVIRA SYNDROME, UTERUS
  • Ankara Üniversitesi Adresli: Evet

Özet

Herlyn-Werner-Wunderlich syndrome is an unusual congenital anomaly of the female genitourinary system, which is described as uterine didelphys with Obstructed Hemi-vagina and Ipsilateral Renal Anomaly (OHIRA), also known as OHVIRA syndrome. Typical symptoms are pelvic pain, tenderness, pelvic mass due to blood collection in the obstructed hemi-vagina and uterus, and dysmenorrhea that usually begins shortly after menarche. Clinical suspicion is very important for diagnosis and correct management avoids both short- and long-term complications. Surgical removal of the vaginal septum is the main treatment method. Herein, we describe the evaluation and surgical management of a patient with OHVIRA syndrome who was diagnosed using magnetic resonance imaging and pelvic ultrasound.