Akademik Veri Yönetim Sistemi
Anestezi Dergisi, cilt.16, sa.2, ss.106-109, 2008 (Scopus)
Skeletal dysplasias are characterized by abnormalities of cartilage and bone growth. Achondroplasia is the most common nonlethal skeletal dysplasia and it is also the most common cause of dwarfism. The estimated frequency of achondroplasia is between 1/15,000 and 1/40,000 live births. The characteristics are a large protruding forehead, large head, depressed nasal bridge, short maxilla, large mandible, large tongue, tonsil enlargement, nasal/pharyngeal/laryngeal hypoplasia, thoracolumbar kyphosis and lumbar hyperlordosis. Neurologic dysfunction due to cervicomedullary compression, thoracolumbar spinal stenosis and scoliosis can also be seen in these patients. Obstructive sleep apnoea (OSA) is prevalent in a large percentage of patients with acondroplasia. The most important breathing disorder during sleep in these patients is upper airway obstruction. Adenoidectomy is an effective treatment for upper airway obstruction and using bilateral tympanostomy tubes is effective for otitis media with effusion. The airway and anesthetic management of these patients poses a significant challenge mainly because of associated anatomic difficulties. In this report, we discuss the anesthetic management of a patient with achondroplasia who underwent adenoidectomy and bilateral ear surgery.