Successful living-related liver transplantation in a child with familial yellow nail syndrome and fulminant hepatic failure: Report of a case

KULOĞLU Z., Uestuendag G., TUNA KIRSAÇLIOĞLU C., KANSU TANCA A., Bingol-Kologlu M., Vargun R., ...Daha Fazla

PEDIATRIC TRANSPLANTATION, cilt.12, sa.8, ss.906-909, 2008 (SCI-Expanded) identifier identifier identifier

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 12 Sayı: 8
  • Basım Tarihi: 2008
  • Doi Numarası: 10.1111/j.1399-3046.2008.00955.x
  • Dergi Adı: PEDIATRIC TRANSPLANTATION
  • Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Sayfa Sayıları: ss.906-909
  • Anahtar Kelimeler: liver transplantation, children, yellow nail syndrome, DUCT BILIARY RECONSTRUCTION, COMPLICATIONS, SIBLINGS
  • Ankara Üniversitesi Adresli: Evet

Özet

An 11-yr-old boy with familial YNS and FHF and who underwent LRLT is presented. LRLT was performed from his father with YNS. The findings of hepatic failure resolved immediately after LRLT, but severe respiratory complications and chylous ascites were observed during the follow-up. At 12 months after successful LT, the patient has good graft function, but findings of YNS including chronic cough, lymphedema and yellow nails are still present. To the best of our knowledge, this is the first case of YNS who underwent LRLT for FHF.