Hereditary pancreatitis: Report of a family from Turkey


KANSU TANCA A., Girgin N., Yurdaydin C., Cetinkaya H., Uzunalimoglu O.

ACTA PAEDIATRICA JAPONICA, cilt.40, sa.6, ss.612-615, 1998 (SCI-Expanded) identifier identifier identifier

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 40 Sayı: 6
  • Basım Tarihi: 1998
  • Doi Numarası: 10.1111/j.1442-200x.1998.tb02001.x
  • Dergi Adı: ACTA PAEDIATRICA JAPONICA
  • Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Sayfa Sayıları: ss.612-615
  • Anahtar Kelimeler: abdominal pain, childhood, chronic pancreatitis, hereditary pancreatitis, PSEUDOCYSTS, MANAGEMENT
  • Ankara Üniversitesi Adresli: Evet

Özet

Chronic pancreatitis is a rare disease in children and is usually secondary to underlying diseases such as hereditary pancreatitis, cystic fibrosis, hyperlipidemia, prolonged malnutrition, gallstones or anomalies of the biliary-pancreatic duct system. Hereditary pancreatitis is a common cause of chronic pancreatitis in children but is often unrecognized until months or years later. We report hen a family with hereditary pancreatitis in which four members are affected.