Anesthesia for a 16-month-old patient with Prader-Willi syndrome

MEÇO B. C., Alanoglu Z., Cengiz O. S., ALKIŞ N.

Journal of Anesthesia, cilt.24, sa.6, ss.949-950, 2010 (SCI-Expanded) identifier identifier

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 24 Sayı: 6
  • Basım Tarihi: 2010
  • Doi Numarası: 10.1007/s00540-010-1005-3
  • Dergi Adı: Journal of Anesthesia
  • Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Sayfa Sayıları: ss.949-950
  • Anahtar Kelimeler: Anesthesia, Hypotonia, Prader-Willi syndrome
  • Ankara Üniversitesi Adresli: Evet

Özet

Prader-Willi syndrome (PWS) is a rare disorder of chromosome abnormalities in which the paternal genes in chromosome 15 are lacking. The clinical course is characterized by hypotonia, hyperphagia, and morbid obesity. Both general and regional anesthesia in these patients is difficult due to morbid obesity and hypotonia. We report our anesthetic management in a patient with PWS with a body mass index (BMI) of 29.43 kg/m2 who underwent orchiopexy and hypospadias repair. The clinical course of the patient was uneventful during the procedure and postoperative period. However, arrangements with a pediatric intensive care setting for the postoperative period are recommended for patients with PWS undergoing surgery. © 2010 Japanese Society of Anesthesiologists.