Subacute sclerosing panencephalitis with an atypical presentation: A case report
Journal of Pediatric Neurology, vol.9, no.1, pp.127-130, 2011 (Scopus)
- Publication Type: Article / Article
- Volume: 9 Issue: 1
- Publication Date: 2011
- Doi Number: 10.3233/jpn-2010-0449
- Journal Name: Journal of Pediatric Neurology
- Journal Indexes: Scopus
- Page Numbers: pp.127-130
- Keywords: atypical presentation, chorea, non-convulsive status epilepticus, SSPE
- Ankara University Affiliated: Yes
Abstract
Subacute sclerosing panencephalitis is almost always fatal with a varying clinical course of illness. It is characterized by slow progression and rarely manifests with a fulminant and rapid course. Atypical presentations such as generalized seizures, visual loss, hemiparesis, non-convulsive status epilepticus and isolated extrapyramidal symptoms can be observed rarely. We report an 11-year-old boy presenting with atypical symptoms initially such as complex partial seizures, chorea and electrographic status epilepticus. The patient was lost within 5 months, which is suitable for a fulminant course. Children presenting with atypical acute or subacute neurologic symptoms should be examined for subacute sclerosing panencephalitis, especially if they have no risk factors for hereditary neurodegenerative and/or neurometabolic diseases. © 2011 - IOS Press and the authors. All rights reserved.