Subacute sclerosing panencephalitis with an atypical presentation: A case report
Journal of Pediatric Neurology, cilt.9, sa.1, ss.127-130, 2011 (Scopus)
- Yayın Türü: Makale / Tam Makale
- Cilt numarası: 9 Sayı: 1
- Basım Tarihi: 2011
- Doi Numarası: 10.3233/jpn-2010-0449
- Dergi Adı: Journal of Pediatric Neurology
- Derginin Tarandığı İndeksler: Scopus
- Sayfa Sayıları: ss.127-130
- Anahtar Kelimeler: atypical presentation, chorea, non-convulsive status epilepticus, SSPE
- Ankara Üniversitesi Adresli: Evet
Özet
Subacute sclerosing panencephalitis is almost always fatal with a varying clinical course of illness. It is characterized by slow progression and rarely manifests with a fulminant and rapid course. Atypical presentations such as generalized seizures, visual loss, hemiparesis, non-convulsive status epilepticus and isolated extrapyramidal symptoms can be observed rarely. We report an 11-year-old boy presenting with atypical symptoms initially such as complex partial seizures, chorea and electrographic status epilepticus. The patient was lost within 5 months, which is suitable for a fulminant course. Children presenting with atypical acute or subacute neurologic symptoms should be examined for subacute sclerosing panencephalitis, especially if they have no risk factors for hereditary neurodegenerative and/or neurometabolic diseases. © 2011 - IOS Press and the authors. All rights reserved.