Camptodactyly-arthropathy-coxa vara-pericarditis (CACP) syndrome

Tasar M., EYİLETEN Z., Kasimzade F., UÇAR T., KENDİRLİ T., Uysalel A.

TURKISH JOURNAL OF PEDIATRICS, cilt.56, sa.6, ss.684-686, 2014 (SCI-Expanded) identifier identifier identifier

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 56 Sayı: 6
  • Basım Tarihi: 2014
  • Dergi Adı: TURKISH JOURNAL OF PEDIATRICS
  • Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Sayfa Sayıları: ss.684-686
  • Anahtar Kelimeler: pericarditis, familial arthropathy, camptodactyly
  • Ankara Üniversitesi Adresli: Evet

Özet

Camptodactyly-arthropathy-coxa vara-pericarditis (CACP) syndrome is a rare autosomal recessive congenital disorder that includes childhood-onset camptodactyly, synovial hyperplasia-related arthropathy, progressive coxa vara deformity and noninflammatory pericarditis. A seven-year-old male patient had a diagnosis of CACP. He had pericardial effusion and underwent surgical tube drainage. CACP syndrome is seen very rarely, and differential diagnosis is very important. CACP is usually treated medically, but surgery may sometimes be preferred, as in our patient.