ANCA positive pauci-immune glomerulonephritis as presenting feature of mantle cell lymphoma: A case report and review of literature Glomerulonefritis pauciinmune ANCA positiva como manifestación inicial de linfoma de células del manto: Informe de un caso y revisión de la literatura
Nefrologia, vol.46, no.1, 2026 (Scopus)
- Publication Type: Article / Article
- Volume: 46 Issue: 1
- Publication Date: 2026
- Doi Number: 10.1016/j.nefroe.2025.501363
- Journal Name: Nefrologia
- Journal Indexes: Scopus
- Keywords: Anti-neutrophil cytoplasmic antibody, Mantle cell lymphoma, Pauci-immune cresentic glomerulonephritis, Rapidly progressive glomerulonephritis
- Ankara University Affiliated: Yes
Abstract
Kidney involvement in mantle cell lymphoma is rare. We report a case of mantle cell lymphoma diagnosed after rapidly progressive glomerulonephritis with biopsy-proven paraneoplastic anti-neutrophil cytoplasmic antibody positive pauci-immune cresentic glomerulonephritis. Lymphoma treatment resulted in improved kidney function. This report demonstrates that pauci-immune cresentic glomerulonephritis can cause kidney impairment as the initial manifestation of mantle cell lymphoma. Physicians should be aware of the atypical presentations of the disease.