Akademik Veri Yönetim Sistemi
British Journal of Radiology, cilt.67, sa.794, ss.207-209, 1994 (SCI-Expanded)
Lipoid proteinosis is a rare generalized disease with autosomal recessive inheritance. It most often involves the skin and mucosal membranes of the aerodigestive tract; but also involves the central nervous system, lung, lymph nodes and striated muscles. We present the computed tomography findings in the cranium and larynx of two siblings with lipoid proteinosis.