Anesthetic Management of a Patient with Pompe Disease: Our Experiment

ARPACI A. H., Venedik O. K.

GAZI MEDICAL JOURNAL, cilt.28, sa.3, ss.208-209, 2017 (ESCI, Scopus, TRDizin) identifier identifier

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 28 Sayı: 3
  • Basım Tarihi: 2017
  • Doi Numarası: 10.12996/gmj.2017.61
  • Dergi Adı: GAZI MEDICAL JOURNAL
  • Derginin Tarandığı İndeksler: Emerging Sources Citation Index (ESCI), Scopus, TR DİZİN (ULAKBİM)
  • Sayfa Sayıları: ss.208-209
  • Anahtar Kelimeler: Pompe disease, sedoanalgesia, monitorized anesthesia care
  • Ankara Üniversitesi Adresli: Evet

Özet

Pompe disease is a fatal autosomal recessive glicogen storage disease presenting with hypertrophic cardiomyopathy, widespread myopathy and hypotonia. In this presentation, we aimed to present our anesthetic approach to 12 teeth extraction planned non-cooperative, 34-month-old patient who were being followed-up in an external center with Infantile Pompe Disease.