Anesthetic Management of a Patient with Pompe Disease: Our Experiment

ARPACI A. H., Venedik O. K.

GAZI MEDICAL JOURNAL, vol.28, no.3, pp.208-209, 2017 (ESCI) identifier identifier

  • Publication Type: Article / Article
  • Volume: 28 Issue: 3
  • Publication Date: 2017
  • Doi Number: 10.12996/gmj.2017.61
  • Journal Name: GAZI MEDICAL JOURNAL
  • Journal Indexes: Emerging Sources Citation Index (ESCI), Scopus, TR DİZİN (ULAKBİM)
  • Page Numbers: pp.208-209
  • Keywords: Pompe disease, sedoanalgesia, monitorized anesthesia care
  • Ankara University Affiliated: Yes

Abstract

Pompe disease is a fatal autosomal recessive glicogen storage disease presenting with hypertrophic cardiomyopathy, widespread myopathy and hypotonia. In this presentation, we aimed to present our anesthetic approach to 12 teeth extraction planned non-cooperative, 34-month-old patient who were being followed-up in an external center with Infantile Pompe Disease.