Clinical Features and HSCT Outcome for SCID in Turkey

İKİNCİOĞULLARI K. A., ÇAĞDAŞ AYVAZ D. N., DOĞU E. F., Tugrul T., Karasu G., Haskologlu S., ...More

JOURNAL OF CLINICAL IMMUNOLOGY, vol.39, no.3, pp.316-323, 2019 (SCI-Expanded) identifier identifier identifier

  • Publication Type: Article / Article
  • Volume: 39 Issue: 3
  • Publication Date: 2019
  • Doi Number: 10.1007/s10875-019-00610-x
  • Journal Name: JOURNAL OF CLINICAL IMMUNOLOGY
  • Journal Indexes: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Page Numbers: pp.316-323
  • Keywords: Severe combined immune deficiency (SCID), Hematopoietic stem cell transplantation (HSCT), clinical features, outcome, STEM-CELL TRANSPLANTATION, SEVERE COMBINED IMMUNODEFICIENCY, IMMUNE RECONSTITUTION, SINGLE-CENTER, COHORT
  • Ankara University Affiliated: Yes

Abstract

Severe combined immunodeficiency (SCID) is the most serious PID, characterized by T cell lymphopenia and lack of antigen-specific T cell and B cell immune responses, inevitably leading to death within the first year of life if hematopoietic stem cell transplantation (HSCT) is not performed.