Successful living-related liver transplantation in a child with familial yellow nail syndrome and fulminant hepatic failure: Report of a case

KULOĞLU Z., Uestuendag G., TUNA KIRSAÇLIOĞLU C., KANSU TANCA A., Bingol-Kologlu M., Vargun R., ...More

PEDIATRIC TRANSPLANTATION, vol.12, no.8, pp.906-909, 2008 (SCI-Expanded) identifier identifier identifier

  • Publication Type: Article / Article
  • Volume: 12 Issue: 8
  • Publication Date: 2008
  • Doi Number: 10.1111/j.1399-3046.2008.00955.x
  • Journal Name: PEDIATRIC TRANSPLANTATION
  • Journal Indexes: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Page Numbers: pp.906-909
  • Keywords: liver transplantation, children, yellow nail syndrome, DUCT BILIARY RECONSTRUCTION, COMPLICATIONS, SIBLINGS
  • Ankara University Affiliated: Yes

Abstract

An 11-yr-old boy with familial YNS and FHF and who underwent LRLT is presented. LRLT was performed from his father with YNS. The findings of hepatic failure resolved immediately after LRLT, but severe respiratory complications and chylous ascites were observed during the follow-up. At 12 months after successful LT, the patient has good graft function, but findings of YNS including chronic cough, lymphedema and yellow nails are still present. To the best of our knowledge, this is the first case of YNS who underwent LRLT for FHF.