Testis sparing surgery for steroid unresponsive testicular tumors of the congenital adrenal hyperplasia

Tiryaki T., AYCAN Z., Hucumenoglu S., Atayurt H.

PEDIATRIC SURGERY INTERNATIONAL, cilt.21, sa.10, ss.853-855, 2005 (SCI-Expanded) identifier identifier identifier

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 21 Sayı: 10
  • Basım Tarihi: 2005
  • Doi Numarası: 10.1007/s00383-005-1547-x
  • Dergi Adı: PEDIATRIC SURGERY INTERNATIONAL
  • Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Sayfa Sayıları: ss.853-855
  • Anahtar Kelimeler: congenital adrenal hyperplasia, testicular adrenal rest tumors, REST TUMORS
  • Ankara Üniversitesi Adresli: Hayır

Özet

The association between testicular tumors/nodules and congenital adrenal hyperplasia (CAH) has been recognized for many years. Tumors are considered to be an aberrant adrenal tissue that has descended with the testes and has become hyperplastic due to ACTH stimulation. The recommended treatment consists of increasing the glucocorticoid dose to suppress ACTH secretions. If the testicular size is not reduced after suppression therapy or a side effect of glucocorticoid dose is noted, surgical intervention should be considered. We diagnosed steroid unresponsive testicular tumors of the CAH in two patients who were treated by testicular sparing tumor enucleation. We believe that testis sparing surgery is the procedure of choice for all patients with testicular adrenal rest tumor, since it maximizes future fertility potential.